γ氨基丁酸转氨酶抗体
规格：1mg/1ml
英文名： ABAT
别名： mitochondrial; (S) 3 amino 2 methylpropionate transaminase; (S)-3-amino-2-methylpropionate transaminase; 4 aminobutyrate aminotransferase; 4 aminobutyrate aminotransferase, mitochondrial; 4-aminobutyr
分子量： 56kDa
储存液：0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glyce
克隆类型：Polyclonal
亚型：IgG
纯化方法：affinity purified by Protein A
**原：KLH conjugated synthetic peptide derived from human ABAT
交叉反应：Human, Mouse, Rat, Pig, Cow, Horse,
细胞定位：细胞浆
γ氨基丁酸转氨酶抗体产品介绍：background: Catalyzes the conversion of gamma-aminobutyrate and L-beta-aminoisobutyrate to succinate semialdehyde and methylmalonate semialdehyde, respectively. Can also convert delta-aminovalerate and beta-alanine. Function: Catalyzes the conversion of gamma-aminobutyrate and L-beta-aminoisobutyrate to succinate semialdehyde and methylmalonate semialdehyde, respectively. Can also convert delta-aminovalerate and beta-alanine. Subunit: Homodimer; disulfide-linked. Subcellularγ氨基丁酸转氨酶抗体Location: Mitochondrion matrix. Tissue Specificity: Liver > pancreas > brain > kidney > heart > placenta. DISEASE: Defects in ABAT are a cause of gamma-aminobutyrate transaminase deficiency (GABA-AT deficiency) [MIM:613163]. The phenotypeγ氨基丁酸转氨酶抗体 of this deficiency includes psychomotor retardation, hypotonia, hyperreflexia, lethargy, refractory seizures, and EEG abnormalities. Similarity: Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
γ氨基丁酸转氨酶抗体产品应用：WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500 （石蜡切片需做抗原修复） not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
研究领域：肿瘤 **学 神经生物学 信号转导
储存条件： Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
来源： Rabbit
外观： Lyophilized or Liquid