酰基辅酶A脱氢酶中链抗体
规格：1mg/1ml
英文名： ACADM
别名： mitochondrial antibody; ACAD 1; ACAD1; Acyl coenzyme A dehydrogenase; Acyl coenzyme A dehydrogenase C 4 to C 12 straight chain; MCAD; MCADH; Medium chain acyl CoA dehydrogenase; Medium chain fatty acy
分子量： 47kDa
储存液：0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glyce
克隆类型：Polyclonal
亚型：IgG
纯化方法：affinity purified by Protein A
**原：KLH conjugated synthetic peptide derived from human ACADM
交叉反应：Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit,
细胞定位：细胞浆 线粒体
酰基辅酶A脱氢酶中链抗体产品介绍：background: ACADM protein is a medium chain specific (C4 to C12 straight chain) acyl Coenzyme A dehydrogenase. The enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. ACADM expression is induced during periods of fasting, when reliance on fatty acids for energy is increased. Clinical phenotypes are associated with ACADM hereditary deficiency. Function: This enzyme is specific for acyl chain lengths of 4 to 16. Subunit: Homotetramer. Interacts with the heterodimeric electron transfer flavoprotein ETF. Subcellular Location: Mitochondrion matrix. DISEASE: Acyl-CoA dehydrogenase medium-chain 酰基辅酶A脱氢酶中链抗体deficiency (ACADMD) [MIM:201450]: An inborn error of mitochondrial fatty acid beta-oxidation which causes fasting hypoglycemia, hepatic dysfunction and encephalopathy, often resulting in death in infancy. Note=The disease is caused by mutations affecting the gene represented in this entry. Similarity: Belongs to the acyl-CoA dehydrogenase family. Gene ID: 34 Database links: Entrez Gene: 酰基辅酶A脱氢酶中链抗体505968 Cow Entrez Gene: 34 Human Entrez Gene: 11364 Mouse Entrez Gene: 24158 Rat Omim: 607008 Human SwissProt: Q3SZB4 Cow SwissProt: P11310 Human SwissProt: P45952 Mouse SwissProt: P08503 Rat Unigene: 445040 Human Unigene: 10530 Mouse Unigene: 6302 Rat Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
酰基辅酶A脱氢酶中链抗体产品应用：WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500 （石蜡切片需做抗原修复） not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
研究领域：肿瘤 细胞生物 **学 转录调节因子 线粒体
储存条件： Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
来源： Rabbit
外观： Lyophilized or Liquid