磷酸半乳糖尿苷酸转移酶1抗体
规格:1mg/1ml
英文名: GALT
别名: Gal 1 P uridylyltransferase; Galactose 1 phosphate uridyl transferase; Galactose 1 phosphate uridylyltransferase; UDP glucose hexose 1 phosphate uridylyltransferase; GALT_HUMAN.
分子量: 43kDa
储存液:0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glyce
克隆类型:Polyclonal
亚型:IgG
纯化方法:affinity purified by Protein A
**原:KLH conjugated synthetic peptide derived from human GALT
交叉反应:Human, Mouse, Rat, Cow,
细胞定位:
磷酸半乳糖尿苷酸转移酶1抗体产品介绍:background: GALT (Galactose 1 phosphate uridyl transferase) catalyzes the second step of the Leloir pathway of galactose metabolism, namely the conversion of UDP glucose + galactose 1 phosphate to glucose 1 phosphate + UDP galactose. The absence of this enzyme results in classic galactosemia in humans and can be fatal in the newborn period if lactose is not removed from the diet. The pathophysiology of galactosemia has not been clearly defined. Subunit: Homodimer (Probable). 磷酸半乳糖尿苷酸转移酶1抗体DISEASE: Defects in GALT are the cause of galactosemia (GALCT) [MIM:230400]. Galactosemia is an inherited disorder of galactose metabolism that causes jaundice, cataracts, and mental retardation. Similarity: Belongs to the galactose-1-phosphate磷酸半乳糖尿苷酸转移酶1抗体 uridylyltransferase type 1 family. Database links: UniProtKB/Swiss-Prot: P07902.3 Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
磷酸半乳糖尿苷酸转移酶1抗体产品应用:WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500 (石蜡切片需做抗原修复) not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
研究领域:肿瘤 细胞生物 **学 激酶和磷酸酶
储存条件: Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
来源: Rabbit
外观: Lyophilized or Liquid