精氨酸tRNA连接酶2抗体
规格：1mg/1ml
英文名： RARS2
别名： arginine tRNA ligase; arginyl tRNA synthetase 2 mitochondrial; Arginyl tRNA synthetase; Arginyl-tRNA synthetase; ArgRS; DALRD2; mitochondrial; PCH6; Probable arginine tRNA ligase; probable arginine tR
分子量： 66kDa
储存液：Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M
克隆类型：Polyclonal
亚型：IgG
纯化方法：affinity purified by Protein A
**原：KLH conjugated synthetic peptide derived from human RARS2
交叉反应：Human, Mouse, Cow,
细胞定位：细胞浆
精氨酸tRNA连接酶2抗体产品介绍：background: The protein encoded by this gene is an arginyl-tRNA synthetase that is found in the mitochondrial matrix. Defects in this gene are a cause of pontocerebellar hypoplasia type 6 (PCH6). [provided by RefSeq, Oct 2008] Subcellular Location: Mitochondrion matrix. Similarity: Belongs to the class-I aminoacyl-tRNA synthetase family. Database links: Entrez Gene: 525894 Cow Entrez Gene: 57038 Human Omim: 611524 Human SwissProt: Q0P5H7 Cow SwissProt: Q5T160 Human Unigene: 16559 Cow Unigene: 精氨酸tRNA连接酶2抗体485910 Human Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. Defects in RARS2 are the cause of pontocerebellar hypoplasia type 6 (PCH6) [MIM:611523]; also known as 精氨酸tRNA连接酶2抗体fatal infantile encephalopathy with mitochondrial respiratory chain defects. Pontocerebellar hypoplasia (PCH) is a heterogeneous group of disorders characterized by an abnormally small cerebellum and brainstem.
精氨酸tRNA连接酶2抗体产品应用：WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500 （石蜡切片需做抗原修复） not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
研究领域：发育生物学 神经生物学 表观遗传学
储存条件： Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
来源： Rabbit
外观： Lyophilized or Liquid