琥珀酸脱氢酶的组合因子1抗体
规格：1mg/1ml
英文名： SDHAF1
别名： LYR motif containing 8; LYR motif-containing protein 8; LYRM8; mitochondrial; SDH assembly factor 1; SDHAF1; SDHF1_HUMAN; Succinate dehydrogenase assembly factor 1; Succinate dehydrogenase assembly fa
分子量： 21kDa
储存液：0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glyce
克隆类型：Polyclonal
亚型：IgG
纯化方法：affinity purified by Protein A
**原：KLH conjugated synthetic peptide derived from human SDHAF1
交叉反应：Human,
细胞定位：
琥珀酸脱氢酶的组合因子1抗体产品介绍：background: The succinate dehydrogenase (SDH) complex (or complex II) of the mitochondrial respiratory chain is composed of 4 individual subunits. The protein encoded by this gene resides in the mitochondria, and is essential for SDH assembly, but does not physically associate with the complex in vivo. Mutations in this gene are associated with SDH-defective infantile leukoencephalopathy (mitochondrial complex II deficiency).[provided by RefSeq, Mar 2010] Function: Plays an essential role in succinate dehydrogenase complex (SDH) assembly, a complex involved in complex II of the mitochondrial electron transport chain. Probably acts by participating in mitochondrial biosynthesis of iron-sulfur centers for complex II. Subcellular Location: Mitochondrion matrix. Tissue Specificity: Ubiquitously expressed. 琥珀酸脱氢酶的组合因子1抗体DISEASE: Mitochondrial complex II deficiency Similarity: Belongs to the complex I LYR family. SDHAF1 subfamily. Gene ID: 644096 Database links: Entrez Gene: 644096 Human Entrez Gene: 68332 Mouse Entrez Gene: 100912030 Rat Entrez Gene: 琥珀酸脱氢酶的组合因子1抗体499125 Rat Omim: 612848 Human SwissProt: A6NFY7 Human SwissProt: Q3U276 Mouse SwissProt: B0K036 Rat Unigene: 356460 Human Unigene: 6844 Mouse Unigene: 3527 Rat Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
琥珀酸脱氢酶的组合因子1抗体产品应用：WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500 （石蜡切片需做抗原修复） not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
研究领域：细胞生物 神经生物学
储存条件： Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
来源： Rabbit
外观： Lyophilized or Liquid